Susac syndrome: clinical features
Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .
Susac syndrome: clinical features. This is a precapillary arteriolar microangiopathy. Fully referenced neurology checklist.
Pathology
- This is a precapillary arteriolar microangiopathy
- There are anti-endothelial cell antibodies (AECA) in 25% of cases
Demographic features
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Diagnostic criteria
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Clinical patterns
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Neurological features
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Ophthalmological features
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Otological features
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Dermatological features
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Other features
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Differential diagnosis
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References
- Susac JO, Egan RA, Rennebohm RM, Lubow M. Susac's syndrome: 1975-2005 microangiopathy/autoimmune endotheliopathy. J Neurol Sci 2007; 257:270-272.
- Turc G, Monnet D, Dupin N, et al. Skin involvement in Susac's syndrome. J Neurol Sci 2011; 305:152-255.
- Susac J, Murtagh FR, Egan A, et al. MRI findings in Susac's syndrome. Neurology 2003; 61:1783-1787.
- Ferretti F, Gereveni S, Colombo B, et al. Susac's syndrome as HIV-associated immune reconstitution inflammatory syndrome. AIDS Res Ther 2013; 10:22.
- Kleffner I, Dorr J, Ringelstein M, et al; for the European Susac Consortium (EuSaC). Diagnostic criteria for Susac syndrome. JNNP 2016; 87:1287-1295.
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