Rapidly progressive dementia
Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .
Rapidly progressive dementia. Prion diseases, Whipple’s disease, Tuberculosis, Neurosyphilis, HIV and other viruses. Fully referenced neurology checklist.
Infective causes
- Prion diseases
- Whipple’s disease
- Tuberculosis
- Neurosyphilis
- HIV and other viruses
- Cryptococcus and other fungi
- Septic encephalopathy
- Subacute sclerosing panencephalitis (SSPE)
Neurodegenerative causes
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Autoimmune and inflammatory causes
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Systemic causes
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Metabolic causes
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Leukodystrophies
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Toxic causes
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Neoplastic causes
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Vascular causes
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Other causes
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References
- Geschwind MD, Shu H, Haman A, Sejvar JJ, Miller BL. Rapidly progressive dementia. Ann Neurol 2008; 64:97-108.
- Josephs KA, Ahlskog JE, Parisi JE, et al. Rapidly progressive neurodegenerative dementias. Arch Neurol 2009; 66:201-207.
- Grau-Rivera O, Gelpi E, Nos C, et al; Neurological Tissue Bank Collaborative Group. Clinicopathological Correlations and Concomitant Pathologies in Rapidly Progressive Dementia: A Brain Bank Series. Neurodegener Dis 2015; 15:350-360.
- Hermann P, Zerr I. Rapidly progressive dementias - aetiologies, diagnosis and management. Nat Rev Neurol 2022 (Online ahead of print).
- Hermann P, Zerr I. Rapidly progressive dementias - aetiologies, diagnosis and management. Nat Rev Neurol 2022; 18:363-376.
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