Rapidly progressive dementia

Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .

Rapidly progressive dementia. Prion diseases, Whipple’s disease, Tuberculosis, Neurosyphilis, HIV and other viruses. Fully referenced neurology checklist.

Infective causes

  • Prion diseases
  • Whipple’s disease
  • Tuberculosis
  • Neurosyphilis
  • HIV and other viruses
  • Cryptococcus and other fungi
  • Septic encephalopathy
  • Subacute sclerosing panencephalitis (SSPE)

Neurodegenerative causes

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Autoimmune and inflammatory causes

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Systemic causes

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Metabolic causes

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Leukodystrophies

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Toxic causes

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Neoplastic causes

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Vascular causes

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Other causes

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References

  1. Geschwind MD, Shu H, Haman A, Sejvar JJ, Miller BL. Rapidly progressive dementia. Ann Neurol 2008; 64:97-108.
  2. Josephs KA, Ahlskog JE, Parisi JE, et al. Rapidly progressive neurodegenerative dementias. Arch Neurol 2009; 66:201-207.
  3. Grau-Rivera O, Gelpi E, Nos C, et al; Neurological Tissue Bank Collaborative Group. Clinicopathological Correlations and Concomitant Pathologies in Rapidly Progressive Dementia: A Brain Bank Series. Neurodegener Dis 2015; 15:350-360.
  4. Hermann P, Zerr I. Rapidly progressive dementias - aetiologies, diagnosis and management. Nat Rev Neurol 2022 (Online ahead of print).
  5. Hermann P, Zerr I. Rapidly progressive dementias - aetiologies, diagnosis and management. Nat Rev Neurol 2022; 18:363-376.
  6. And 13 more. Subscribe to see the full list

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