Parry Romberg syndrome (PRS): systemic features
Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .
Parry Romberg syndrome (PRS): systemic features. This is an autoimmune dysplasia of facial skin and subcutaneous tissues.
Pathology
- This is an autoimmune dysplasia of facial skin and subcutaneous tissues
- It causes slowly progressive unilateral facial atrophy
- 5-10% may become bilateral
Epidemiology
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Craniofacial features
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Ophthalmic features
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Synonyms
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References
- Tolkachjov SN, Patel NG, Tollefson MM. Progressive hemifacial atrophy: a review. Orphanet J Rare Dis 2015; 10:39.
- Wong M, Phillips CD, Hagiwara M, Shatzkes DR. Parry Romberg syndrome: 7 cases and literature review. Am J Neuroradiol 2015; 36:1355-1361.
- Miller MT, Sloane H, Goldberg MF, Grisolano J, Frenkel M, Mafee MF. Progressive hemifacial atrophy (Parry-Romberg disease). J Pediatr Ophthalmol Strabismus 1987; 24:27-36.
- Vix J, Mathis S, Lacoste M, Guillevin R, Neau JP. Neurological manifestations in Parry-Romberg syndrome: 2 Case reports. Medicine (Baltimore) 2015; 94:e1147.
- Aydın H, Yologlu Z, Sargın H, Metin MR. Parry-Romberg syndrome. Physical, clinical, and imaging features. Neurosciences (Riyadh) 2015; 20:368-371.
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