Orthostatic myoclonus (OM)

Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .

Orthostatic myoclonus (OM). Atypical parkinsonism, Alzheimer's disease (AD), Normal pressure hydrocephalus (NPH). Fully referenced neurology checklist.

Causes

  • Atypical parkinsonism
  • Alzheimer's disease (AD)
  • Normal pressure hydrocephalus (NPH)
  • Cerebral amyloid angiopathy (CAA)
  • Chronic renal failure
  • Autoimmune with Caspr2 antibodies

Clinical features

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Differential diagnosis

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Electromyography (EMG)

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References

  1. Erro R, Bhatia KP, Cordivari C. Shaking on standing: a critical review. Mov Disord Clin Pract 2014; 1:173-179.
  2. Gövert F, Witt K, Erro R, et al. Orthostatic myoclonus associated with Caspr2 antibodies. Neurology 2016; 86:1353-1355.
  3. van Gerpen JA. A retrospective study of the clinical and electrophysiological characteristics of 32 patients with orthostatic myoclonus. Parkinsonism Relat Disord 2014; 20:889-893. 
  4. Glass GA, Ahlskog JE, Matsumoto JY. Orthostatic myoclonus: a contributor to gait decline in selected elderly. Neurology 2007; 68:1826-1830.
  5. Gasca-Salas C, Arcocha J, Artieda J, Pastor P. Orthostatic myoclonus: an underrecognized cause of unsteadiness? Parkinsonism Relat Disord 2013; 19:1013-1017.

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