IgG4-related disease: management
Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .
IgG4-related disease: management. Serum IgG4 levels are elevated. Fully referenced neurology checklist.
Blood tests
- Serum IgG4 levels are elevated
Imaging
Locked: subscribe to see this section.
Cerebrospinal fluid (CSF) analysis
Locked: subscribe to see this section.
Histopathology
Locked: subscribe to see this section.
Treatment
Locked: subscribe to see this section.
Treatment of refractory cases with Rituximab
Locked: subscribe to see this section.
References
- Huijbers MG, Querol LA, Niks EH, et al. The expanding field of IgG4-mediated neurological autoimmune disorders. Eur J Neurol 2015; 22:1151-1161.
- Dalmau J. Name a brain protein, and an autoantibody shall be found! Neurol Neuroimmunol Neuroinflamm 2015; 2:e159.
- Massey J. IgG4-related hypertrophic pachymeningitis coexpressing antineutrophil cytoplasmic antibodies. Neurol Neuroimmunol Neuroinflamm. 2017; 4:e341.
- Baptista B, Casian A, Gunawardena H, D'Cruz D, Rice CM. Neurological Manifestations of IgG4-Related Disease. Curr Treat Options Neurol 2017; 19:14.
- Taniguchi T, Hamasaki A, Okamoto M. A case of suspected lymphocytic hypophysitis and organizing pneumonia during maintenance therapy for autoimmune pancreatitis associated with autoimmune thrombocytopenia. Endocr J 2006; 53:563-566.
- And 5 more. Subscribe to see the full list
