Episodic ataxia (EA): differential diagnosis
Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .
Episodic ataxia (EA): differential diagnosis. Basilar migraine, Familial hemiplegic migraine (FHM). Fully referenced neurology checklist.
Neurological differentials
- Basilar migraine
- Familial hemiplegic migraine (FHM)
- Paroxysmal dyskinesia
- Post ictal state
- Spinocerebellar ataxia: especially SCA 6
- Periodic vestibulo-cerebellar ataxia
Metabolic differentials
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References
- Jen JC, Graves TD, Hess EJ, et al. Primary episodic ataxias: diagnosis, pathogenesis and treatment. Brain 2007; 130:2484-2493.
- Brazis PW, Masdeu JC, Biller J. Localization in Clinical Neurology. Lippincott Williams & Wilkins 2007. Philadelphia p372.
- Debray FG, Lambert M, Gagne R, et al. Pyruvate dehydrogenase deficiency presenting as intermittent isolated acute ataxia. Neuropediatrics 2008; 39:20-23.