Dermatomyositis with vascular pathology (DM-VP)

Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .

Dermatomyositis with vascular pathology (DM-VP). Interstitial lung disease, Raynaud’s phenomenon, Mechanic's hands. Fully referenced neurology checklist.

Clinical features

  • Interstitial lung disease
  • Raynaud’s phenomenon
  • Mechanic's hands
  • Arthralgias

Investigations

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Differential diagnosis

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Treatment

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References

  1. Bucelli RC, Pestronk A. Immune myopathies with perimysial pathology: Clinical and laboratory features. Neurol Neuroimmunol Neuroinflamm 2018; 5:e434.

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