Cystic fibrosis (CF): management

Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .

Cystic fibrosis (CF): management. Polysomnography, Echocardiography, Evoked potentials. Fully referenced neurology checklist.

Neurological investigations

  • Polysomnography
  • Magnetic resonance imaging (MRI) brain: increased gray matter density
  • Echocardiography
  • Evoked potentials

Systemic investigations

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Treatment

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References

  1. Reznikov LR. Cystic fibrosis and the nervous system. Chest 2017; 151:1147-1155.
  2. Roy B, Woo MS, Vacas S, Eshaghian P, Rao AP, Kumar R. Regional brain tissue changes in patients with cystic fibrosis. J Transl Med 2021; 19:419.
  3. Shakkottai A, Nasr SZ, Hassan F, Irani S, O'Brien LM, Chervin RD. Sleep-disordered breathing in cystic fibrosis. Sleep Med 2020; 74:57-65. 
  4. Sritippayawan S, MacLaughlin EF, Woo MS. Acute neurological deficits in a young adult with cystic fibrosis. Pediatr Pulmonol 2003; 35:147-151.
  5. Katsouli G, Polytarchou A, Tsaoussoglou M, Loukou I, Chrousos G, Kaditis AG. Nocturnal oximetry in children with obstructive lung disease or sleep-disordered breathing. Pediatr Pulmonol 2019; 54:551-556. 
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