Chorea: neurological causes

Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .

Chorea: neurological causes. Huntington's disease (HD), Huntington’s disease like 2 (HD like-2). Fully referenced neurology checklist.

Genetic

  • Huntington's disease (HD)
  • Huntington’s disease like 2 (HD like-2)
  • Dentatorubral-pallidoluysian atrophy (DRPLA)
  • Spinocerebellar ataxia (SCA): SCA2, SCA3, SCA7
  • Neuroacanthocytosis
  • Neuroferritinopathy
  • Ataxia telangiectasia
  • Benign hereditary chorea
  • Paroxysmal kinesigenic choreoathetosis
  • Ataxia with oculomotor apraxia (AOA)
  • Pantothenate kinase-associated neurodegeneration (PKAN)
  • Wilson’s disease
  • Neimann Pick type C (NPC)
  • Dopa-responsive dystonia (DRD)
  • Mitochondrial disease
  • Fragile X tremor ataxia syndrome (FXTAS)
  • ANO3-related chorea-dystonia

Infective

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Focal brain lesions

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Other causes

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References

  1. Cardoso F, Seppi K, Mair KJ, Wenning GK, Poewe W. Seminar on choreas. Lancet Neurol 2006; 5:589-602.
  2. Ropper AH, Brown RH. Principles of Neurology Eigth edition. McGraw Hill New York 2005 p64.
  3. Wild EJ, Tabrizi SJ. The differential diagnosis of chorea. Pract Neurol 2007; 7:360-373.
  4. Galea I, Norwood F, Phillips MJ, Shearman C, McMonagle P, Gibbs WR. Pearls and oy-sters: resolution of hemichorea following endarterectomy for severe carotid stenosis. Neurology 2008; 71:e80-e83.
  5. Brazis PW, Masdeu JC, Biller J. Localization in Clinical Neurology. Lippincott Williams & Wilkins 2007 Philadelphia p427.
  6. And 7 more. Subscribe to see the full list

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