Cerebral amyloid angiopathy related inflammation (CAAri)
Written and reviewed by Dr Ibrahim Imam, Consultant Neurologist. Last reviewed .
Cerebral amyloid angiopathy related inflammation (CAAri). Rapid cognitive decline, Headaches, Seizures. Fully referenced neurology checklist.
Clinical features
- Rapid cognitive decline
- Headaches
- Seizures
- Impaired consciousness
- Behavioural change
- Focal neurological deficits
- It may be asymptomatic
Magnetic resonance imaging (MRI): white matter hyperintensities
Locked: subscribe to see this section.
Magnetic resonance imaging (MRI): other features
Locked: subscribe to see this section.
Cerebrospinal fluid (CSF) analysis
Locked: subscribe to see this section.
Other investigations
Locked: subscribe to see this section.
Differential diagnosis
Locked: subscribe to see this section.
Immunosuppressant treatment
Locked: subscribe to see this section.
Prognosis
Locked: subscribe to see this section.
References
- Auriel E, Charidimou A, Gurol ME, et al. Validation of clinicoradiological criteria for the diagnosis of cerebral amyloid angiopathy-related inflammation. JAMA Neurol 2016; 73:197-202.
- Mendonça MD, Caetano A, Pinto M, Cruz e Silva V, Viana-Baptista M. Stroke-like episodes heralding a reversible encephalopathy: microbleeds as the key to the diagnosis of cerebral amyloid angiopathy-related inflammation-a case report and literature review. J Stroke Cerebrovasc Dis 2015; 24:e245-250.
- Salvarani C, Morris JM, Giannini C, Brown RD Jr, Christianson T, Hunder GG. Imaging findings of cerebral amyloid angiopathy, aβ-related angiitis (ABRA), and cerebral amyloid angiopathy-related inflammation: a single-institution 25-year experience. Medicine (Baltimore) 2016; 95:e3613.
- Martín-Jiménez P, Sánchez-Tornero M, Llamas-Velasco S, et al. Cerebral amyloid angiopathy-related inflammation: clinical features and treatment response in a case series. Neurologia (Engl Ed) 2023 Jul 10:S2173-5808(23)00041-X.
- Bravo GÁ, Cirera LS, Torrentà LR. Clinical and radiological features of cerebral amyloid angiopathy-related inflammation. Neurol Sci 2021 (Online ahead of print).
- And 6 more. Subscribe to see the full list
